Th1-skewed profile and excessive production of proinflammatory cytokines in a NFKB1-deficient patient with CVID and severe gastrointestinal manifestations

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Détails bibliographiques
Publié dans:Clinical immunology (Orlando, Fla.). - 1999. - 195(2018) vom: 15. Okt., Seite 49-58
Auteur principal: Dieli-Crimi, Romina (Auteur)
Autres auteurs: Martínez-Gallo, Mónica, Franco-Jarava, Clara, Antolin, Maria, Blasco, Laura, Paramonov, Ida, Semidey, Maria E, Álvarez Fernández, Antoni, Molero, Xavier, Velásquez, Julio, Martín-Nalda, Andrea, Pujol-Borrell, Ricardo, Colobran, Roger
Format: Article en ligne
Langue:English
Publié: 2018
Accès à la collection:Clinical immunology (Orlando, Fla.)
Sujets:Case Reports Journal Article Research Support, Non-U.S. Gov't Autoinflammation Common Variable Immunodeficiency Enteropathy NF-κB pathway NFKB1 NOD2 Next Generation Sequencing plus... Primary Immunodeficiency Th1 cells Cytokines Inflammation Mediators NF-kappa B NOD2 protein, human Nod2 Signaling Adaptor Protein