Optimizing outcomes of hematopoietic stem cell transplantation for severe combined immunodeficiency

This FOCIS Centers of Excellence Short Analytical Review is based on the clinical vignette of two boys from the same family with very different outcomes following hematopoietic stem cell transplantation (HSCT) for X-linked severe combined immunodeficiency (SCID). We review the kinetics of immune rec...

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Détails bibliographiques
Publié dans:Clinical immunology (Orlando, Fla.). - 1999. - 131(2009), 2 vom: 27. Mai, Seite 179-88
Auteur principal: Cuvelier, Geoff D E (Auteur)
Autres auteurs: Schultz, Kirk R, Davis, Jeff, Hirschfeld, Aaron F, Junker, Anne K, Tan, Rusung, Turvey, Stuart E
Format: Article en ligne
Langue:English
Publié: 2009
Accès à la collection:Clinical immunology (Orlando, Fla.)
Sujets:Case Reports Journal Article Review IL2RG protein, human Interleukin Receptor Common gamma Subunit
Description
Résumé:This FOCIS Centers of Excellence Short Analytical Review is based on the clinical vignette of two boys from the same family with very different outcomes following hematopoietic stem cell transplantation (HSCT) for X-linked severe combined immunodeficiency (SCID). We review the kinetics of immune reconstitution following HSCT in SCID and emphasize the latest information regarding optimizing transplant outcomes for this disorder. The cases illustrate the difficulties and controversies surrounding the optimal strategies for planning SCID transplants. Specifically, we will focus on 3 areas of current debate and investigation: (i) factors involved in donor selection; (ii) the role of pretransplant conditioning; and (iii) benefits of early HSCT for SCID
Description:Date Completed 15.05.2009
Date Revised 13.04.2009
published: Print-Electronic
Citation Status MEDLINE
ISSN:1521-7035
DOI:10.1016/j.clim.2009.01.003